Mauriac Syndrome in the Age of Newer Insulin Analogues
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چکیده
The authors describe a five year-old plump looking female child with poorly controlled type 1 diabetes mellitus, hepatomegaly and growth retardation. Contrary to the usual phenotype of thin emaciated appearance in type 1 diabetes mellitus, the presence of above features should make one suspect Mauriac syndrome. Since the basis of this syndrome is poor metabolic control, early recognition is important. The authors emphasize the importance of optimal glycaemic control in preventing complications associated with Mauriac syndrome.
منابع مشابه
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تاریخ انتشار 2017